Kasabach-Merritt Phenomenon: Classic Presentation and Management Options
نویسندگان
چکیده
منابع مشابه
Kasabach-Merritt Phenomenon: Classic Presentation and Management Options
Kasabach-Merritt phenomenon (KMP) is a rare consumptive coagulopathy associated with specific vascular tumors, kaposiform hemangioendothelioma, and tufted angioma. Kasabach-Merritt phenomenon, characterized by profound thrombocytopenia, hypofibrinogenemia, elevated fibrin split products, and rapid tumor growth, can be life-threatening. Severe symptomatic anemia may also be present. With prompt ...
متن کامل[Kaposiform haemangioendothelioma with Kasabach-Merritt phenomenon].
Kasabach-Merritt phenomenon is a serious coagulopathy associated with kaposiform hemangioendothelioma (KHE), tufted angioma, and possibly other vascular neoplasms. KHE presenting in the absence of Kasabach-Merritt phenomenon is rare, although tufted angioma frequently occurs without thrombocytopenia. We retrospectively reviewed 10 cases of KHE without Kasabach-Merritt phenomenon. The tumors app...
متن کاملKasabach–Merritt phenomenon and prenatal counseling: a case series
Kasabach-Merritt phenomenon can be encountered in the perinatal period. No consensus exists regarding prenatal management. We report one prenatal case leading to therapeutic abortion and one neonatal case, successfully treated by a multimodal therapy. Prenatal counseling should include the possibility of neonatal multimodal treatment that can lead to favorable outcomes.
متن کاملKasabach-Merritt phenomenon in a neonatal kaposiform haemangioendothelioma.
To cite: Mardegan V, Doglioni N, De Bernardo G, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2014205855 DESCRIPTION A female infant was born at 27 weeks of gestation through emergency caesarean section, performed because of an acute increase of a compressive thoracic malformation diagnosed at the 20th gestational week. At birth, two enormous violaceous m...
متن کاملTufted angioma associated with Kasabach-Merritt phenomenon: a therapeutic challenge.
Fig. 1. (A) Tufted angioma involving the chin in a one-month-old child. (B) The patient at 2 months of age showing a subtle increase in tumour size and decrease in platelet count. (C) A subtle residual lesion on the chin of the patient at the age of 5 years. Tufted angioma (TA) is an infrequently seen, benign vascular tumour, which was first described in 1949 (1). It is characterized clinically...
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ژورنال
عنوان ژورنال: Clinical Medicine Insights: Blood Disorders
سال: 2017
ISSN: 1179-545X,1179-545X
DOI: 10.1177/1179545x17699849